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Year : 2014  |  Volume : 10  |  Issue : 2  |  Page : 428-430

Idiopathic renal replacement lipomatosis: A rare renal pseudo tumor

Department of Pathology, Indira Gandhi Medical College, Shimla, Himachal Pradesh, India

Correspondence Address:
Shailja P Wahal
Department of Pathology, Indira Gandhi Medical College, Shimla, Himachal Pradesh - 171 001
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Source of Support: None, Conflict of Interest: None

DOI: 10.4103/0973-1482.136680

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Renal replacement lipomatosis (RRL) is a rare condition that occurs as an end result of renal atrophy or destruction of renal parenchyma by excessive lipomatous tissue in renal sinus and perinephric space. We report a case of RRL presenting as a right renal mass clinically. Intra-venous pyelography and renal scan revealed a left non-functioning kidney. A left nephrectomy was performed. After histopathological examination and extensive literature search, a diagnosis of RRL was given. In majority of cases, it is associated with renal calculi. Idiopathic variety is not common. It is a rare entity and the diagnosis may be missed due to lack of experience. It has to be differentiated from other fat-containing tumors such as renal lipoma, xanthogranulomatous pyelonephritis, angiomyolipoma and liposarcoma.

Abstract in Chinese

特发性肾脏替代性脂肪过多症:一种罕见的肾脏假性肿瘤 摘要 肾脏替代性脂肪过多症(RRL)是一种因肾窦和肾周空间脂肪组织过多最终引发肾萎缩、肾实质破坏的罕见情况。我们报告一个表现为右侧肾脏肿块的RRL临床病例。静脉肾盂造影、肾扫描显示左肾无功能。行左肾切除术。组织病理学检查和广泛的文献搜索后,诊断为RRL。在大多数病例伴有肾结石相关。特发性变化是不常见的。它是一种罕见的实体,可能因经验不足而误诊。它需要区别于其他含脂肪的肿瘤如肾脂肪瘤,黄色肉芽肿肾盂肾炎,血管平滑肌脂肪瘤、脂肪肉瘤。 关键词:特发性,肾脏替代性脂肪过多症,肾脏的

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